PMID: 17586695

Poschet JF, Timmins GS, Taylor-Cousar JL, Ornatowski W, Fazio J, Perkett E, Wilson KR, Yu HD, de Jonge HR, Deretic V
Pharmacological modulation of cGMP levels by phosphodiesterase 5 inhibitors as a therapeutic strategy for treatment of respiratory pathology in cystic fibrosis.
Am J Physiol Lung Cell Mol Physiol. 2007 Sep;293(3):L712-9. Epub 2007 Jun 22., [PubMed]
Sentences
No. Mutations Sentence Comment
39 ABCC7 p.Trp1282*
X
ABCC7 p.Trp1282* 17586695:39:81
status: NEW
view ABCC7 p.Trp1282* details
IB3-1 is a bronchial epithelial cell line derived from a CF patient with a DF508/W1282X CFTR mutant genotype (55). Login to comment